lnflammatory Myopathies in Childhood | 2003, Volume 9 - Issue 1

Hatice KARASOY, Ahmet GÖKÇAY, Ayfer ÜLKÜ

Ege Üniversitesi Tıp Fakültesi Nöroloji Anabilim Dalı. [email protected]

Keywords: Dermatomyositis, polymyositis, inclusion body myositis, childhood.

Abstract

ldiopathic inflammatory myopathies are a group of heterogenous diseases of unknown patogenesis and are characterized by mononuclear cell infiltration in muscle. Three majorsubsets have been identified: Dermatomyositis (DM), polimyositis (PM) and inclusion body myositis (IBM). DM and PM are rare but IBM is exceptionally rare in childhood. We reviewed clinical features and prognosis of 11 patients with PM, 6 patients with DM and 1 patient with IBM. At the begining, their clinical pictures were quite similar except skininvolvement, but prognosis was different. Prognosis was better in DM group, moderate in PM group and worst in IBM case.