İbrahim AYDOĞDU1, Veli ÇITIŞLI2, Ayşın KISABAY1, Safiye BİLGİN1, Gökhan KESER3, Sacit ŞEN4

1Ege Üniversitesi Tıp Fakültesi Nöroloji ABD. [email protected]
2Ege Üniversitesi Tıp Fakültesi Nöroşirurji ABD
3Ege Üniversitesi Tıp Fakültesi Romatoloji BD
4Ege Üniversitesi Tıp Fakültesi Patoloji ABD

Keywords: Churg-Strauss syndrome, vasculitis, peripheral neuropathy, mononeuritis multiplex.

Abstract

Churg-Strauss syndrome (CSS) is a rare systemic necrotising vasculitis affecting small sized vessels characterised by asthma, sinusitis, pulmonary infiltrations, hypereosinophilia, and peripheral neuropathy. Peripheral neuropathy or mononeuritis multiplex is most common neurological feature of CSS and sometimes may be the only manifestation of the underlying vasculitic disease. In this paper, we report a case of 48 years old patient who presenting progressive severe asymetrical polyneuropathy as major feature of disease besides other clinical findings of systemic vasculitis.