Erdheim-Chester Disease Presented with Bilateral Carotid Artery Occlusion: Case Report
Yahya Çelik1, Kemal Balcı1, Talip Asil1, Erdem Tüzün2, Mustafa Kemal Hamamcıoğlu3, Osman Temizöz4, Sait Albayram5, Aydın Sav6
1Department of Neurology, Faculty of Medicine, University of Trakya, Edirne, Turkey
2Department of Neurology, Faculty of Istanbul Medicine, University of Istanbul, Istanbul, Turkey
3Department of Neurosurgery, Faculty of Medicine, University of Trakya, Edirne, Turkey
4Department of Radiology, Faculty of Medicine, University of Trakya, Edirne, Turkey
5Department of Radiology, Faculty of Cerrahpasa Medicine, University of Istanbul, Istanbul, Turkey
6Deparment of Pathology, Faculty of Medicine, University of Marmara, Istanbul, Turkey
Keywords: Erdheim-Chester disease, ophthalmoplegia, carotid arteries.
Abstract
Erdheim-Chester disease is a rare, non-Langerhans form of systemic histiocytosis of unknown etiology. The disease affects multiple organ systems, including musculoskeletal, cardiac, pulmonary, gastrointestinal, and central nervous systems, producing protean manifestations. Neurological manifestations are less frequent. We present a 44-year-old patient with Erdheim-Chester disease who had bilateral carotid artery occlusion and cavernous sinus infiltration.