Sultan TARLACI, Ayşe SAĞDUYU ÖZKAYA, Hadiye ŞİRİN

Ege Üniversitesi Tıp Fakültesi, Nöroloji Anabilim Dalı, İzmir

Keywords: Creutzfeldt-jakob disease, clinical diagnostic criteria.

Abstract

Creutzfeldt -jakob disease as being the most common one among the other rare priondisesase, is characterised with progressive demans, myoclonic jerks and a variety of othervisual and neurological abnormalities. Twelve patients with the diagnosis ofCreutzfeldt-]akob disease were evaluated, ten of whom retrospectively and the restprospectively, according to the clinical, radiological and pathological findings. Diagnosticvalue of the clinical features is discussed in the view of the literature.