Neuromyelitis Optica:  Case Report

Deniz Tuncel; Ebru Özay; Canan Yücesan; Nursel Aydın

Deniz Tuncel, Ebru Özay, Canan Yücesan, Nursel Aydın

Department Of Neurology, Ankara University Faculty Of Medicine, Ankara, Turkey

Keywords: Devic’s syndrome, diagnostic criteria

Abstract

OBJECTIVES: Neuromyelitis optica (Devic’s syndrome) is an uncommon but severe form of demyelinating disease. This syndrome is characterized by acute or relapsing inflammatory demyelination restricted to the optic nerves and spinal cord. We present a patient with monophacic Devic’s syndrome according to Dean Wingerchuk and et al. diagnostic criteria (2006).

MATERIAL-METHODS: A 26-year-old woman was admitted in our hospital with acute visual lost and tetraplegia. There were demyelination in MRI that involved cervicomeduller junction to thoracal 5 level and bilateral optic nerves. The cerebrospinal fluid included mild pleocytosis and raised protein level. Oligoclonal band was absent. In the blood examinations, immunological and enfectious markers was negative.

RESULTS: The patient had been treated with corticosteroid, plasma exchange and intravenous immunglobuline respectively.

CONCLUSION: The clinic was less recovery and stable for 6 years.