The Neurophysiologic Frequency of Hereditary Neuropathy with Liability to Pressure Palsy in Entrapment NeuropathiesF Gökçem Yıldız1, Gülay Nurlu2, Sevim Erdem Özdamar2, Çağrı Mesut Temuçin2
1Hacettepe University Institute of Neurological Sciences and Psychiatry, Ankara, Turkey
2Hacettepe University Faculty of Medicine, Department of Neurology, Ankara, Turkey
Objective: Hereditary neuropathy with liability to pressure palsy (HNPP) needs to be differentiated from entrapment neuropathies due to differences in the treatment management.Keywords: Hereditary neuropathy with liability to pressure palsy, entrapment neuropathy, peripheral myelin protein 22
Materials and Methods: Among 5075 patients with entrapment neuropathy, we retrospectively evaluated the neurophysiologic results of 20 patients with three or more entrapments.
Results: Ten patients were diagnosed as having HNPP according to their genetic or nerve biopsy results; eight (80%) had bilateral Carpal tunnel syndrome, nine (90%) had bilateral ulnar entrapment neuropathy, eight (80%) had bilateral median and ulnar entrapment together; and three (30%) had one-sided peroneal neuropathy.
Conclusion: Our data suggest that analyzing the neurophysiologic studies and keeping HNPP in mind are essential to characterize underdiagnosed patients with HNPP referred for entrapment neuropathy.
F Gökçem Yıldız, Gülay Nurlu, Sevim Erdem Özdamar, Çağrı Mesut Temuçin. The Neurophysiologic Frequency of Hereditary Neuropathy with Liability to Pressure Palsy in Entrapment Neuropathies. Turk J Neurol. 2016; 22(4): 177-180
Corresponding Author: F Gökçem Yıldız, Türkiye